Idiopathic pulmonary hemosiderosis in an adult patient responded well to corticosteroid therapy.

نویسندگان

  • Omer Deniz
  • Onder Ongürü
  • Fatih Ors
  • Seyfettin Gümüş
  • Ergun Tozkoparan
  • Hayati Bilgiç
  • Kudret Ekiz
چکیده

Idiopathic pulmonary hemosiderosis (IPH) is a very rare disorder of unknown etiology characterized by recurrent or chronic hemorrhage and accumulation of hemosiderin in the lung parenchyma. It is most common in children but can occur in adults. Clinical manifestations of the disease include iron deficiency anemia without any known cause, pulmonary symptoms such as hemoptysis, dyspnea and cough, and parenchymal lesions on chest X-ray. The clinical course of the disease may vary from patient to patient however, in general, the prognosis of the disease is worse. Treatment is symptomatic and supportive. Corticosteroids and other immune suppressive agents were used for the therapy of IPH. Since it is seen rarely in adults and the clinical course of the disease vary from patient to patient we presented an adult male patient with IPH responded well to steroid therapy clinically and radiologically.

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عنوان ژورنال:
  • Tuberkuloz ve toraks

دوره 55 1  شماره 

صفحات  -

تاریخ انتشار 2007